Introduction: The coexistence of inguinal hernias and ureteroceles in pediatric patients is a rare occurrence. Management of both conditions must take into consideration the possibility of additional associated urological anomalies.
This case highlights the importance of a thorough exam and using a multidisciplinary approach to the treatment of a patient with right-sided multicystic dysplastic kidney disease who presented with a right ureterocele and right inguinal hernia.
Case Presentation: A four-year and four-month-old male with known right-sided multicystic dysplastic kidney disease, right-sided hydroureteronephrosis, and a recently discovered right ureterocele, presented to the clinic for a newly developed bulge in his right groin extending into the right scrotum. Physical examination and imaging confirmed the presence of a reducible inguinal hernia, a persistent right-sided ureterocele, and compensatory hypertrophy of the left kidney.
The patient underwent a concurrent right inguinal hernia repair and transurethral puncture and drainage of the ureterocele under general anesthesia. The postoperative course was complicated by mild scrotal swelling and discomfort, suggesting a possible testicular hematoma, which was managed conservatively.
Discussion: This case highlights the importance of consistent and timely imaging, intervention, and evaluation of patients with congenital urological anomalies. Independently, inguinal hernias and ureteroceles are common in the pediatric population. However, their concurrent presentation in patients with MCDK is rare, requiring prompt surgical repair to prevent future complications, including urinary tract obstructions or incarcerated hernias. Successful diagnosis, repair, and recovery also depend on effective communication among providers, parents, and patients.

